Efficacy of intravenous immunoglobulin in shrinking lung syndrome associated with mixed connective tissue disease: a case report

António, Manuel; Khmelinskii, Nikita; Fonseca, João Eurico

http://hdl.handle.net/10451/53241

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Authors

António, Manuel

Khmelinskii, Nikita

Fonseca, João Eurico

Abstract(s)

Shrinking lung syndrome is a rare manifestation of connective tissue diseases, namely systemic lupus erythematosus. It is characterised by reduced lung volumes and extra-pulmonary restrictive ventilatory pattern with good response to high-dose glucocorticoids alone or in combination with a second immunosuppressive agent. Here, we describe a case associated with mixed connective tissue disease and effectively treated with intravenous immunoglobulin.