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Idiopathic inflammatory myopathies : state of the art on clinical practice guidelines

2019Artigo científico Acesso aberto
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dc.contributor.authorMeyer, Alain
dc.contributor.authorScirè, Carlo Alberto
dc.contributor.authorTalarico, Rosaria
dc.contributor.authorAlexander, Tobias
dc.contributor.authorAmoura, Zahir
dc.contributor.authorAvcin, Tadej
dc.contributor.authorBarsotti, Simone
dc.contributor.authorBeretta, Lorenzo
dc.contributor.authorBlagojevic, Jelena
dc.contributor.authorBurmester, Gerd
dc.contributor.authorCavazzana, Ilaria
dc.contributor.authorCherrin, Patrick
dc.contributor.authorDamian, Laura
dc.contributor.authorDoria, Andrea
dc.contributor.authorFonseca, João Eurico
dc.contributor.authorFurini, Federica
dc.contributor.authorGaletti, Ilaria
dc.contributor.authorHoussiau, Frederic
dc.contributor.authorKrieg, Thomas
dc.contributor.authorLarosa, Maddalena
dc.contributor.authorLaunay, David
dc.contributor.authorCampanilho-Marques, Raquel
dc.contributor.authorMartin, Thierry
dc.contributor.authorMatucci-Cerinic, Marco
dc.contributor.authorMoinzadeh, Pia
dc.contributor.authorMontecucco, Carlomaurizio
dc.contributor.authorMoraes-Fontes, Maria Francisca
dc.contributor.authorMouthon, Luc
dc.contributor.authorNeri, Rossella
dc.contributor.authorPaolino, Sabrina
dc.contributor.authorPiette, Yves
dc.contributor.authorRednic, Simona
dc.contributor.authorTamirou, Farah
dc.contributor.authorTincani, Angela
dc.contributor.authorToplak, Natasa
dc.contributor.authorBombardieri, Stefano
dc.contributor.authorHachulla, Eric
dc.contributor.authorMueller-Ladner, Ulf
dc.contributor.authorSchneider, Matthias
dc.contributor.authorSmith, Vanessa
dc.contributor.authorVieira, Ana
dc.contributor.authorCutolo, Maurizio
dc.contributor.authorMosca, Marta
dc.contributor.authorCavagna, Lorenzo
dc.date.accessioned2021-03-10T16:32:25Z
dc.date.available2021-03-10T16:32:25Z
dc.date.issued2019
dc.description© Author(s) (or their employer(s)) 2019. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJpt_PT
dc.descriptionThis article has been corrected since it first published. The authors would like to notify that title of the article has been changed to:Idiopathic inflammatory myopathies: state of the art on clinical practice guidelines. RMD Open 2019;5:e000784corr1. doi:10.1136/rmdopen-2018-000784corpt_PT
dc.description.abstractIdiopathic inflammatory myopathies (IIMs) encompass a heterogeneous group of rare autoimmune diseases characterised by muscle weakness and inflammation, but in antisynthetase syndrome arthritis and interstitial lung disease are more frequent and often inaugurate the disease. Clinical practice guidelines (CPGs) have been proposed for IIMs, but they are sparse and heterogeneous. This work aimed at identifying: i) current available CPGs for IIMs, ii) patients’ and clinicians’ unmet needs not covered by CPGs. It has been performed in the framework of the European Reference Network on rare and complex connective tissue and musculoskeletal diseases (ReCONNET), a network of centre of expertise and patients funded by the European Union’s Health Programme. Fourteen original CPGs were identified, notably recommending that: i) extra-muscular involvements should be assessed; ii) corticosteroids and methotrexate or azathioprine are first-line therapies of IIMs. iii) IVIG is a treatment of resistantDM that may be also used in other resistant-IIMs; iv) physical therapy and sun protection (in DM patients) are part of the treatment; v) tumour screening for patients with DM include imaging of chest, abdomen, pelvis and breast (in woman) along with colonoscopy (in patients over 50 years); vi) disease activity and damages should be monitor using standardised and validated tools. Yet, only half of these CPGs were evidence-based. Crucial unmet needs were identified both by patients and clinicians. In particular, there was a lack of large multidisciplinary working group and of patients’ preferences. The following fields were not or inappropriately targeted: diagnosis; management of extra-muscular involvements other than skin; co-morbidities and severe manifestations.pt_PT
dc.description.sponsorshipThis publication was funded by the European Union’s Health Programme (2014-2020), Framework Partnership Agreement number: 739531 – ERN ReCONNET. The content of this publication represents the views of the authors only and it is their sole responsibility; it cannot be considered to reflect the views of the European Commission and/or the Consumers, Health, Agriculture and Food Executive Agency (CHAFEA) or any other body of the European Union. The European Commission and the Agency do not accept any responsibility for use that may be made of the information it contains.pt_PT
dc.description.versioninfo:eu-repo/semantics/publishedVersionpt_PT
dc.identifier.citationRMD Open 2019;4:e000784pt_PT
dc.identifier.doi10.1136/rmdopen-2018-000784pt_PT
dc.identifier.eissn2056-5933
dc.identifier.urihttp://hdl.handle.net/10451/46782
dc.language.isoengpt_PT
dc.peerreviewedyespt_PT
dc.publisherBMJ Publishing Group, Ltd.pt_PT
dc.relation.publisherversionhttps://rmdopen.bmj.com/pt_PT
dc.rights.urihttp://creativecommons.org/licenses/by-nc/4.0/pt_PT
dc.titleIdiopathic inflammatory myopathies : state of the art on clinical practice guidelinespt_PT
dc.typejournal article
dspace.entity.typePublication
oaire.citation.issueSuppl 1pt_PT
oaire.citation.titleRMD Openpt_PT
oaire.citation.volume4pt_PT
person.familyNameFonseca
person.familyNameCampanilho-Marques
person.familyNameMoraes-Fontes
person.givenNameJoão
person.givenNameRaquel
person.givenNameMaria Francisca
person.identifier.ciencia-idF310-B85D-57C7
person.identifier.ciencia-idFB1D-B9BA-5204
person.identifier.ciencia-id791A-696C-7248
person.identifier.orcid0000-0003-1432-3671
person.identifier.orcid0000-0002-1894-8516
person.identifier.orcid0000-0002-8917-6592
person.identifier.scopus-author-id7101983519
rcaap.rightsopenAccesspt_PT
rcaap.typearticlept_PT
relation.isAuthorOfPublication1772dc12-7c55-4c76-ae2d-c23270172480
relation.isAuthorOfPublication324a51d2-4ed3-428e-aeb8-0c470a05324d
relation.isAuthorOfPublication1c0556ff-4931-4bc7-bdc4-e643f7a0f97c
relation.isAuthorOfPublication.latestForDiscovery1c0556ff-4931-4bc7-bdc4-e643f7a0f97c

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